Agenesis or abscence of gallbladder and cystic duct, wheter it comes with or without the symptoms of biliary systems, is a rare anomaly. There are less than 200 recorded cases in the world. It can be diagnosed only by surgical exploration and necropsy. Most recorded cases were necropsy findings.
It combines usually other anomalies, such as cardiac anomalies, esophagotracheal fistula, anal imperforation, polycystic kidney or abscence of extrahepatic biliary passage etc. They can not survive more than usually one year. In other cases without other fatal anomalies can live without difficulties. They complain the symptoms of cholecystitis, choledocholithiasis, jaundice and icterus on middle aged life and they can live without difficulties after surgical correction of the cause.
Author experienced a case of the agenesis of the gallbladder and cystic duct with multiple accessary lobes of the liver. The accesary lobes of the liver have no clinical significance except when there are ectopic lobes or torsion of the pedicle on the accesary lobes27), and so, I will report the case and review the literatures about agenesis of the gallbladder and cystic duct.
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